Search on: FAMILIAL ENDOCRINE ADENOMATOSIS 
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Descriptor English:   Multiple Endocrine Neoplasia 
Descriptor Spanish:   Neoplasia Endocrina Múltiple 
Descriptor Portuguese:   Neoplasia Endócrina Múltipla 
Synonyms English:   Adenomatoses, Familial Endocrine
Adenomatoses, Multiple Endocrine
Adenomatosis, Familial Endocrine
Adenomatosis, Multiple Endocrine
Adenopathies, Multiple Endocrine
Adenopathy, Multiple Endocrine
Endocrine Adenomatoses, Familial
Endocrine Adenomatoses, Multiple
Endocrine Adenomatosis, Familial
Endocrine Adenomatosis, Multiple
Endocrine Adenopathies, Multiple
Endocrine Adenopathy, Multiple
Endocrine Neoplasia, Multiple
Endocrine Neoplasms, Multiple
Familial Endocrine Adenomatoses
Familial Endocrine Adenomatosis
Multiple Endocrine Adenomatoses
Multiple Endocrine Adenomatosis
Multiple Endocrine Adenopathies
Multiple Endocrine Adenopathy
Multiple Endocrine Neoplasia Syndromes
Multiple Endocrine Neoplasms
Neoplasia, Multiple Endocrine
Neoplasms, Multiple Endocrine  
Tree Number:   C04.588.322.400
C04.651.600
C04.700.630
C16.320.700.630
C19.344.400
Definition English:   A group of autosomal dominant diseases characterized by the combined occurrence of tumors involving two or more ENDOCRINE GLANDS that secrete PEPTIDE HORMONES or AMINES. These neoplasias are often benign but can be malignant. They are classified by the endocrine glands involved and the degree of aggressiveness. The two major forms are MEN1 and MEN2 with gene mutations on CHROMOSOME 11 and CHROMOSOME 10, respectively. 
Indexing Annotation English:   general or unspecified; prefer specifics; coordinate IM with specific endocrine/neoplasm pre-coordinates (IM) + specific histological type (IM) if pertinent; DF MULTIPLE ENDOCRINE NEOPL
History Note English:   95; was NEOPLASMS, MULTIPLE ENDOCRINE 1983-94; was ADENOMATOSIS, FAMILIAL ENDOCRINE 1965-82 (Prov 1964) 
Allowable Qualifiers English:  
BS blood supply BL blood
CF cerebrospinal fluid CI chemically induced
CH chemistry CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SC secondary SU surgery
TH therapy UL ultrastructure
UR urine VE veterinary
VI virology  
Record Number:   22577 
Unique Identifier:   D009377 

Occurrence in VHL:
 

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